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Adult patients with pulmonary arterial hypertension due to congenital heart disease: a review on advanced medical treatment with bosentan

Pulmonary arterial hypertension (PAH) is a progressive disease with poor survival outcome. PAH is classified by the 2009 updated clinical classification of pulmonary hypertension and a major subgroup is PAH due to congenital heart disease (CHD) with systemic-to-pulmonary shunt. CHD-PAH is a result o...

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Autores principales: Schuuring, Mark J, Vis, Jeroen C, Duffels, Marielle G, Bouma, Berto J, Mulder, Barbara JM
Formato: Artigo
Lenguaje:Inglês
Publicado: Dove Medical Press 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2940744/
https://ncbi.nlm.nih.gov/pubmed/20856682
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