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Functional effects of naturally occurring KCNJ11 mutations causing neonatal diabetes on cloned cardiac K(ATP) channels

ATP-sensitive K(+) (K(ATP)) channels are hetero-octamers of inwardly rectifying K(+) channel (Kir6.2) and sulphonylurea receptor subunits (SUR1 in pancreatic β-cells, SUR2A in heart). Heterozygous gain-of-function mutations in Kir6.2 cause neonatal diabetes, which may be accompanied by epilepsy and...

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Autors principals: Tammaro, Paolo, Proks, Peter, Ashcroft, Frances M
Format: Artigo
Idioma:Inglês
Publicat: Blackwell Science Inc 2006
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1805653/
https://ncbi.nlm.nih.gov/pubmed/16339180
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/jphysiol.2005.099168
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