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Screening for pulmonary arterial hypertension in systemic sclerosis

Pulmonary arterial hypertension (PAH) is a dreaded complication of systemic sclerosis (SSc) that occurs in ∼10% of patients. Most individuals present with severe symptoms, significant functional impairment and severe haemodynamics at diagnosis, and survival after PAH diagnosis is poor. Therefore, ea...

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Bibliografiset tiedot
Päätekijät: Jason Weatherald, David Montani, Mitja Jevnikar, Xavier Jaïs, Laurent Savale, Marc Humbert
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: European Respiratory Society 2019-07-01
Sarja:European Respiratory Review
Linkit:http://err.ersjournals.com/content/28/153/190023.full
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