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Screening for pulmonary arterial hypertension in systemic sclerosis
Pulmonary arterial hypertension (PAH) is a dreaded complication of systemic sclerosis (SSc) that occurs in ∼10% of patients. Most individuals present with severe symptoms, significant functional impairment and severe haemodynamics at diagnosis, and survival after PAH diagnosis is poor. Therefore, ea...
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Autores principales: | , , , , , |
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Formato: | Artigo |
Lenguaje: | Inglês |
Publicado: |
European Respiratory Society
2019-07-01
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Colección: | European Respiratory Review |
Acceso en línea: | http://err.ersjournals.com/content/28/153/190023.full |
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