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Mercaptopurine Treatment in an Adult Man with Orbital and Intracranial Rosai-Dorfman Disease

Background. Rosai-Dorfmann disease (RDD) is a rare, idiopathic non-Langerhans cell histiocytosis, affecting children and young adults, that commonly presents as painless, massive cervical lymphadenopathy with fever, weight loss, and polyclonal hypergammaglobulinemia. Cervical lymphadenopathy and ext...

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Hlavní autoři: Valentina Arnao, Marianna Riolo, Giovanni Savettieri, Paolo Aridon
Médium: Artigo
Jazyk:Inglês
Vydáno: Hindawi Limited 2016-01-01
Edice:Case Reports in Neurological Medicine
On-line přístup:http://dx.doi.org/10.1155/2016/1030478
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