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Treating TNF Receptor Associated Periodic Fever Syndrome in End-Stage Renal Failure

Tumor necrosis factor receptor associated periodic syndrome (TRAPS) is a rare monogenic autoinflammatory disease. Its most severe manifestation is secondary amyloidosis. A 44-year-old male presented with nephrotic syndrome. Kidney biopsy was conclusive for secondary amyloidosis. The patient and his...

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Autores principales: J. Coutinho, R. S. Chorão, M. Oliveira, C. R. Santos
Formato: Artigo
Lenguaje:Inglês
Publicado: Hindawi Limited 2019-01-01
Colección:Case Reports in Nephrology
Acceso en línea:http://dx.doi.org/10.1155/2019/6819476
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